Atrial Rhabdomyoma: A Case Report

Case Report: Primary cardiac tumors are quite rare among children. The incidence of cardiac tumors during fetal life and among children according to echocardiography has been reported to be between 0.14% and 0.08%, respectively. Rhabdomyomas are the most common primary cardiac tumors in children. They comprise more than 60% of all primary cardiac tumors during childhood. Most frequently, they exist in the ventricular walls or cavities. Sometimes they involve the atria or atrioventricular junction. Location in the atrioventricular junction may predispose the patient to arrhythmia and pre-excitation. These tumors are multiple in 90% of the cases. The presenting manifestation depends on the size and site of the mass. Echocardiography is the most accessible diagnostic method, but biopsy has remained the “gold standard” for the proof of the diagnosis. Surgical repair should be considered only for sick patients with unstable hemodynamic because most of these tumors regress spontaneously. In this case report, we describe a 2-year-old boy with atrioventricular junction single mass and progressive mitral regurgitation without any arrhythmia who underwent complete mass resection.