Report of two cases with neonatal Diabetes Mellitus due to pancreas agenesis

Neonatal diabetes divided into transient and permanent forms. Pancreatic agenesis is a very rare cause of permanent neonatal diabetes. In this paper, two male patients with neonatal hyperglycemia are reported. They were very sensitive to insulin and malabsorption syndrome gradually appeared in them. The first patient had hyperglycemia on the third day of life and steatorrhea, edema and anemia appeared during first two months. The second one was brought at 10 days of life but her mother had noted to fatty and frequent stools. Anemia and edema appeared during admission. Sonography in the first patient reported normal pancreas and caused delay in diagnosis, but CT-scan was useful for correct diagnosis in the second patient. Hyperglycemia accompanied by insulin sensitivity, malabsorption signs and symptoms, lack of anomalies and low birth weight should be assumed as pancreas agenesis and CT-scan is useful way for diagnosis.