An Extremely Rare Orbital Tumor

To present a case of orbital granular cell tumor, a rare orbital tumor.Case Report: A 55-year-old woman presented with binocular diplopia and right ocular displacement. The problem had initiated 3 years ago. A firm nontender mass at the region of the right lower lid was visible. Orbital CT-scan disclosed a well-defined mass in the inferior right orbit with involvement of the inferior muscles. Subtotal excision of the mass, and histopathological and immunohistochemical studies revealed granular cell tumor. Postoperatively, there was improvement in patient's signs and symptoms. Because of residual tumor, she was referred for radiotherapy. Immunohistochemical and histopathological studies are beneficial in diagnosis of rare orbital tumors.