Cor triatriatum with pulmonary hypertension: A case report

Çor triatriatum is a cardiac anomaly that is due to failure of resorption of the common pulmonary vein results in a left atrium divided by an abnormal fibromascular diaphragm into posterosuperior and the anteroinferior chambers. The communication between the divided atrial chambers may be large، small or absent، depending on the size of the opening (s) in the diaphragm، which determines the degree of obstruction to pulmonary venous return. Ëlevation of both pulmonary venous pressure and pulmonary vascular resistance may result in sever pulmonary hypertension. Ït may be detected as incidental finding in a patient who has an echocardiogram for another reason. Çases with sever obstruction present similar to patients with congenital pulmonary vein stenosis. We present a case with palpitation and breathlessness. Ëchocardiography revealed fibromascular diaphragm above left atrial appendage and no significant gradient between two chambers. Çatheterization showed moderate to severe pulmonary hypertension. Because of non obstructive Çor triatriatum، surgery was not necessary، follow up by echocardiography recommended.