Clear cell sarcoma of the hand: a case of malignant melanoma of soft parts

A case is reported with clear cell sarcoma (CCS) of the hand. Early diagnosis of clear cell sarcoma is always difficult due to its slow growing nature, benign clinical appearance, lack of pigmentation in most cases, and relatively young age of patients which make it to clinically appear as a benign soft tissue tumor. We report a case of clear cell sarcoma of hand in a 56 year old male with a non-painful, soft tissue tumor. Following suspicious appearance, rapid growth of the tumor and complications due to limited movement of the fingers, it was decided to perform excisional biopsy in order to remove the tumor and perform histological assessment. According to microscopic findings and immunohistochemical results, clear cell sarcoma was diagnosed. Our case reminds that clear cell sarcoma can develop in locations such as hand and upper extremities which are not common places to find it, therefore it is important to consider clear cell sarcoma in differential diagnosis of malignancies in hand and upper extremities.