An infected Hydatid cyst with Budd - chiari syndrome manifestation in Zahedan

Hydatid cyst is among the most common etiologies of hepatic cysts and is caused by Echinococcos granulosus. Dogs are definitive host and human may be infected accidentally. Liver is the most common site of involvement (70%). Generally the cysts remain asymptomatic only if its size expanded too much it causes symptoms such as dyspepsia, a mass in right lower quadrant, pain and other manifestation such as obstructive jaundice and secondary infection.As it is reported here, an infected hydatid cyst in this case became large enough to put pressure on IVC and hepatic vein causing Budd – chiari syndrome. The patient presentation was ascitis and lower limb edema because of portal vein hypertension. After imaging studies she became candidate for operation, and she underwent successful incomplete Liver resection, abscess drainage, hepatoraphe and billiary drainage.