Primary Leiomyosarcoma in the Maxilla: A Case Report

Primary leiomyosarcoma is a rare tumor in the head and neck. This report is to describe a case of maxillary leiomyosarcoma in a 36-year-old man, who was referred to Chamran Hospital (Shiraz, Iran) in September 2009. The patient was diagnosed with leiomyosarcoma, originated in the left premaxilla. Histogenetically, maxillary leiomyosarcoma arise from the medial muscle of blood vessels or from primitive mesenchyme in the maxilla (1). The lesion was treated with surgical resection; Midface Degloving procedure. The primary site received postoperative radiotherapy with external irradiation of 45 GY (25 treatments, 1/8 GY). The patient was monitored at follow-up visits in the next one year.