Main Pulmonary Artery Aneurysm and Fish Mouth Pulmonary Valve: A Case Report

Bicuspid pulmonary valve as a rare cardiac anomaly results in hemodynamic alterations leading to aneurysmal dilation of the pulmonary artery (PA), which has been reported in association with other heart defects. Pulmonic stenosis is usually presented as a part of a complicated disease (e.g. tetralogy of Fallot) or in association with other abnormalities such as corrected transposition of great arteries, although it can be developed as a distinct entity.
The case described in this study was a 36-year-old man with a history of syncope and dyspnea. The complementary studies revealed isolated bicuspid PS and aneurysmally dilated main PA.
Both main PA aneurysm and fish mouth bicuspid pulmonary valve are rare cardiac anomalies that are sometimes presented in association with other heart diseases. Pulmonic stenosis can occur as an isolated anomaly but more often is a part of complex defects. The present report emphasizes the fact that an isolated bicuspid anomaly of the pulmonary valve may be compatible with normal cardiac anatomy and remain uneventful even on its own accord, although our case presented signs and symptoms of severe pulmonic stenosis at the age of 36.