Robotic Excision of the Vagina in a 46 XX DSD Male Patient. First Pediatric Report

The Disorders of Sex Differentiation (DSD) represent a wide range of congenital anomalies of the genitalia. Sur-gical treatment of these cases may become a challenge. We present a case of a 16-year-old boy with 46 XX DSD, SRY negative, presented with persistent dribbling incontinence, recurrent UTI, and perineal pain. Past medical his-tory included right orchiectomy, laparoscopic excision of uterus, fallopian tubes, and left streak gonad at another institution at the age of 2 years. The native vagina was left in place. VCUG confirmed the presence of the residual vagina (8 cm in maximum length), connected with the bulbar urethra. Robotic-assisted laparoscopic excision of the vagina was performed with satisfying short and long-term results.