Breast Dermatofibrosarcoma Protuberans: Report of a Rare Case

Dermatofibrosarcoma protuberans (DFSP) is a rare tumor and has a slow-growing behavior. Presentation is nonspecific, and diagnosis is made after the operation and pathologic examination. The most common sites of this tumor are the trunk, head and neck, and extremities. We report a 42-year-old woman presenting with a breast mass and positive history of breast cancer in her mother. Pre-operation biopsy showed phyllodes tumor. After wide excision of the mass, the pathology report confirmed the DFSP diagnosis. Apart from surgery, she received no adjuvant treatment (chemotherapy, radiotherapy, or hormone therapy). The patient has not experienced recurrence since then. According to the rarity and high rate of recurrence of breast DFSP, it should not be missed as a differential diagnosis of breast masses. Taking a multidisciplinary approach and using proper diagnosis and treatment methods can improve the outcome.