Congenital Macular Macrovessels: A Case Report, Review of the Literature

To report a case of congenital macular macrovessels Case report : An 8-year-old girl was referred for decreased vision in her right eye. Her best corrected visual acuity (BCVA) in the right eye was 20/200 and in the left eye 20/20. Anterior segment examinations were normal in both eyes. Posterior segment examination of the right eye showed abnormal macrovessels crossing the macula and passing over the fovea. Left funduscopy finding was insignificant. Congenital retinal macrovessels are rare anomalies. They are aberrant retinal vessels, usually venules, present in the posterior pole and crossing the avascular foveal region. Most of these cases are unilateral and stable with excellent visual prognosis and are detected on routine examination. Foveal cysts, hemorrhages and displaced foveola may be also associated with this anomaly. These entities must be distinguished from racemose angiomas, capillary hemangiomas of the retina and even when associated with neurological symptoms, should be considered as part of the Wyburn-Masson syndrome. In children with CRM and decreased visual acuity, it should be treated promptly to avoid amblyopia. Regular examination and careful follow-up of vascular lesions is mandatory to limit possible complications.