Idiopathic Retinal Vasculitis, Aneurysms, and Retinitis: A Case Report

To report a case of Idiopathic Retinal Vasculitis, Aneurysm, and Retinitis [IRVAN] with angiographic and optical coherence tomography (OCT) findings.Case Report: A 15-year-old girl with a 2 -month history of decreased visual acuity in both eyes and best corrected visual acuity of 20/70 in both eyes was referred to the retina clinic. Mild inflammation was present in anterior chamber and vitreous cavity. There was severe exudative maculopathy, optic disc swelling, multiple tied knot-like aneurysmal dilations of retinal arterioles, and retinal vasculitis bilaterally. Systemic and laboratory work-up were negative. OCT illustrated severe retinal edema, cystic spaces in nerve fiber layer (NFL), and excrescences on the retinal surface around posterior pole. In this report, we present OCT findings in a case of IRVAN syndrome about which few reports are available. The findings show that reduced axonal conduction and schisis-like cavities in NFL may be present.