Papillon- Lefevre: syndrome: Reconstruction of severly atrophic maxilla and mandible using iliac bonely by Interpositional & Onlay bone graft

Papillon-Lefèvre syndrome is a rare autosomal recessive genetic disorder characterized by palmar-plantar hyperkeratosis, with rapidly progressive periodontitis and premature loss of both deciduous and permanent teeth. This article presents the reconstruction of jaws of a patient with Papillon-Lefèvre syndrome with Iliac bone graft. Case Report: Interpositional graft with Lefort I surgery in maxilla and Onlay bone graft in mandible in a 20-year-old female patient with Papillon-Lefèvre syndrome was done. In our follow-up the bone grafts is clinically stable and no pain or infection was found. The patient continues to be seen at regular follow-up visits. Lefort I procedure and interpositional bone graft for reconstruction of maxillary in Papillon-Lefevre syndrome, make better profile in patients. We not only successfully treated our patient functionally and esthetically in first stage of treatment plane by bone grafting, but also provided psychological benefits to the patient.