Choledochal cyst is a rare problem, defined as congenital dilatation of the biliary tract. There are five particular categories of choledochal cysts with some sub-types. The optimal management is removal of entire extrahepatic biliary system in addition to cholecystectomy and reconstruction by Roux-en-Y hepaticojejunostomy.
We reported a 25 years old patient with a giant choledochal cyst. This Choledochal cyst may belong to subtype 1a plus affecting the intrapancreatic portion of common bile duct (CBD). The cyst was successfully resected without any complications.
Intraoperative finding of choledochal cyst is very important, therefore, knowledge of potential presence of this rare disease and its management with respect to anatomical variations is very important for surgeons