Evaluation of Total Anomalous Pulmonary Vein Connection and Its Outcomes in the Shahid Madani Hospital from 1986 to 2008

Total anomalous pulmonary vein connections are formed 1-3% of all congenital heart disease. There isn’t any priority with respect to the gender. Nowadays total correction is associated with less mortality and morbidity. Obstruction of pulmonary vein maybe is intern sic forms of disease or perhaps it would be the complication of after surgery. All of the neonates and the patients who were admitted in children hospital and all the patients who were admitted in Madani Hospital for surgery and their diagnosed were TAPVC were contained in this study. Diagnoses were on the base of echocardiography and cathetrism and in two cases of them were associated with CT angiography. The age of surgery, associated diseases, syndrome, existing PH, the need for type of TAPVC, existing heart failure after surgery, the period of hospitalization in ICU and the period of using of mechanical respirator and need to a mechanical reventilation, need to long term inotrope after surgery, rhythm of after surgery, existing pulmonary venous obstruction before and after surgery of patients was recorded in questioner. The data was entered to computer by using SPSS software and they were analyzed by using statistical tests T-Test, X2 and one way ANOVA. 23 patients with TAPVC were entered to this study. 16 patients were male and 7 patients were female. 8 patients were dead before the surgery. 15 patients were operated. The average age was 36/29±30/20 months. From the 15 operated patients, 8 patients were supra cardiac in which 4 patient (26.7%) of them returned to SVC (1case returned to azygous vein) and the rest 3 patient (26.7%) returned to left in nominate vein. 4 patients were dead (26.7%). Nowadays the early correction of TAPVC is company with less mortality and morbidity. Using of inhaled Nitric Oxide for controlling of pulmonary hypertension is necessary and we must think about providing for this gas in this hospital. The age of operated patients were high that was because of lately see pediatric cardiologist in higher ages. So it is so necessary to inform the parents about congenital heart disease. Diagnosis and treatment of obstruction of pulmonary (either by intrinsic or extrinsic) veins maybe resolved with resurvey or putting Stent which using of it in this center will be beneficial.